eng Oriental Scientific Publishing Company Biomedical and Pharmacology Journal 0974-6242 2016-08-21 9 2 853 857 10.13005/bpj/1017 8145 article Balachander 1 L. Malathi 1 J. Jenita Jacobina 1 N. Aravindha Babu 1 Department of Oral Pathology, Sree Balaji Dental College and Hospital, Bharath University, Pallikaranai, Chennai – 600100. Gorlin-Goltz syndrome is a rare autosomal dominant disorder with high penetrance and variable expressivity.It involves multiple organ systems.Pathogenesis of this syndrome is attributed to mutations in the PTCH-1gene. Diagnosis of this syndrome is based on major and minor criteria. The most common finding of this syndrome is multiple odontogenic keratocysts in the jaws. Recurrence of this lesion is most characteristic. A case report of33 years male patient with Gorlin-Goltz syndrome is presented here. https://biomedpharmajournal.org/vol9no2/gorlin-goltz-syndrome-nevoid-basal-cell-carcinoma-syndrome-a-case-report/ Calcification of falx cerebri Gorlin-Goltz syndrome  Odontogenic Keratocyst